ARSA Rabbit Polyclonal Antibody (CAB1736)
- SKU:
- CAB1736
- Product Type:
- Antibody
- Reactivity:
- Human
- Mouse
- Host Species:
- Rabbit
- Isotype:
- IgG
- Antibody Type:
- Polyclonal Antibody
- Research Area:
- Cell Biology
Frequently bought together:
Description
Product Name: | ARSA Rabbit Polyclonal Antibody |
SKU: | CAB1736 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human,Mouse |
Immunogen: | Recombinant fusion protein containing a sequence corresponding to amino acids 210-509 of human ARSA (NP_000478.3). |
Sequence: | LMAD AQRQ DRPF FLYY ASHH THYP QFSG QSFA ERSG RGPF GDSL MELD AAVG TLMT AIGD LGLL EETL VIFT ADNG PETM RMSR GGCS GLLR CGKG TTYE GGVR EPAL AFWP GHIA PGVT HELA SSLD LLPT LAAL AGAP LPNV TLDG FDLS PLLL GTGK SPRQ SLFF YPSY PDEV RGVF AVRT GKYK AHFF TQGS AHSD TTAD PACH ASSS LTAH EPPL LYDL SKDP GENY NLLG GVAG ATPE VLQA LKQL QLLK AQLD AAVT FGPS QVAR GEDP ALQI CCHP GCTP RPAC CHCP DPHA |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:500 - 1:2000 |
Synonyms: | ASA; MLD; ARSA |
Positive Sample: | Jurkat,HeLa,HepG2,A-549,Mouse testis,Mouse liver,Mouse brain |
Conjugate: | Unconjugated |
Cellular Localization: | Lysosome. |
Calculated MW: | 54kDa |
Observed MW: | 66kDa |
The protein encoded by this gene hydrolyzes cerebroside sulfate to cerebroside and sulfate. Defects in this gene lead to metachromatic leucodystrophy (MLD), a progressive demyelination disease which results in a variety of neurological symptoms and ultimately death. Alternatively spliced transcript variants have been described for this gene.
Purification Method: | Affinity purification |
Gene ID: | 410 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,50% glycerol,pH7.3. |