Galactosidase alpha (GLA) Rabbit Polyclonal Antibody (CAB13987)
- SKU:
- CAB13987
- Product Type:
- Antibody
- Reactivity:
- Human
- Host Species:
- Rabbit
- Isotype:
- IgG
- Antibody Type:
- Polyclonal Antibody
- Research Area:
- Cell Biology
Frequently bought together:
Description
Product Name: | Galactosidase alpha (GLA) Rabbit Polyclonal Antibody |
SKU: | CAB13987 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human |
Immunogen: | Recombinant fusion protein containing a sequence corresponding to amino acids 150-429 of human Galactosidase alpha (Galactosidase alpha (GLA)) (NP_000160.1). |
Sequence: | GYYD IDAQ TFAD WGVD LLKF DGCY CDSL ENLA DGYK HMSL ALNR TGRS IVYS CEWP LYMW PFQK PNYT EIRQ YCNH WRNF ADID DSWK SIKS ILDW TSFN QERI VDVA GPGG WNDP DMLV IGNF GLSW NQQV TQMA LWAI MAAP LFMS NDLR HISP QAKA LLQD KDVI AINQ DPLG KQGY QLRQ GDNF EVWE RPLS GLAW AVAM INRQ EIGG PRSY TIAV ASLG KGVA CNPA CFIT QLLP VKRK LGFY EWTS RLRS HINP TGTV LLQL ENTM QMSL KDLL |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:500 - 1:2000 |
Synonyms: | GALA; Galactosidase alpha (GLA) |
Positive Sample: | HeLa |
Conjugate: | Unconjugated |
Cellular Localization: | Lysosome. |
Calculated MW: | 49kDa |
Observed MW: | 49kDa |
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
Purification Method: | Affinity purification |
Gene ID: | 2717 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,50% glycerol,pH7.3. |