PAX3 Rabbit Polyclonal Antibody (CAB1675)
- SKU:
- CAB1675
- Product Type:
- Antibody
- Reactivity:
- Human
- Mouse
- Rat
- Host Species:
- Rabbit
- Isotype:
- IgG
- Antibody Type:
- Polyclonal Antibody
- Research Area:
- Cardiovascular
Frequently bought together:
Description
Product Name: | PAX3 Rabbit Polyclonal Antibody |
SKU: | CAB1675 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human,Mouse,Rat |
Immunogen: | Recombinant fusion protein containing a sequence corresponding to amino acids 1-236 of human PAX3 (NP_852122.1). |
Sequence: | MTTL AGAV PRMM RPGP GQNY PRSG FPLE VSTP LGQG RVNQ LGGV FING RPLP NHIR HKIV EMAH HGIR PCVI SRQL RVSH GCVS KILC RYQE TGSI RPGA IGGS KPKQ VTTP DVEK KIEE YKRE NPGM FSWE IRDK LLKD AVCD RNTV PSVS SISR ILRS KFGK GEEE EADL ERKE AEES EKKA KHSI DGIL SERA SAPQ SDEG SDID SEPD LPLK RKQR RSRT TFTA EQLE ELER |
Tested Applications: | WB IHC-P IF/ICC ELISA |
Recommended Dilution: | WB,1:500 - 1:1000 IHC-P,1:50 - 1:200 IF/ICC,1:50 - 1:200 |
Synonyms: | WS1; WS3; CDHS; HUP2; PAX-3; PAX3 |
Positive Sample: | 293T,Rat testis |
Conjugate: | Unconjugated |
Cellular Localization: | Nucleus. |
Calculated MW: | 53kDa |
Observed MW: | 60kDa |
This gene is a member of the paired box (PAX) family of transcription factors. Members of the PAX family typically contain a paired box domain and a paired-type homeodomain. These genes play critical roles during fetal development. Mutations in paired box gene 3 are associated with Waardenburg syndrome, craniofacial-deafness-hand syndrome, and alveolar rhabdomyosarcoma. The translocation t(2;13)(q35;q14), which represents a fusion between PAX3 and the forkhead gene, is a frequent finding in alveolar rhabdomyosarcoma. Alternative splicing results in transcripts encoding isoforms with different C-termini.
Purification Method: | Affinity purification |
Gene ID: | 5077 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,50% glycerol,pH7.3. |