GAA Rabbit Monoclonal Antibody (CAB19234)
- SKU:
- CAB19234
- Product Type:
- Antibody
- Antibody Type:
- Monoclonal Antibody
- Reactivity:
- Human
- Mouse
- Rat
- Host Species:
- Rabbit
- Isotype:
- IgG
- Synonyms:
- GAA
- LYAG
- glucosidase alpha
- acid
- Research Area:
- Cell Biology
Frequently bought together:
Description
Product Name: | GAA Rabbit Monoclonal Antibody |
SKU: | CAB19234 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human |
Immunogen: | A synthetic peptide corresponding to a sequence within amino acids 100-200 of human GAA (P10253). |
Sequence: | QEQC EARG CCYI PAKQ GLQG AQMG QPWC FFPP SYPS YKLE NLSS SEMG YTAT LTRT TPTF FPKD ILTL RLDV MMET ENRL HFTI KDPA NRRY EVPL ETPH V |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:500 - 1:1000 |
Synonyms: | LYAG; GAA |
Positive Sample: | 293T,HepG2,DU145 |
Conjugate: | Unconjugated |
Cellular Localization: | Lysosome, Lysosome membrane. |
Calculated MW: | 105kDa |
Observed MW: | 76kDa/105kDa |
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.
Purification Method: | Affinity purification |
Gene ID: | 2548 |
Clone Number: | ARC2392 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.02% sodium azide,0.05% BSA,50% glycerol,pH7.3. |