G6PC Polyclonal Antibody (CAB21168)
- SKU:
- CAB21168
- Product Type:
- Antibody
- Antibody Type:
- Polyclonal Antibody
- Reactivity:
- Mouse
- Rat
- Applications:
- WB
- Isotype:
- IgG
- Host Species:
- Rabbit
Description
Product Name: | G6PC Polyclonal Antibody |
SKU: | CAB21168 |
Size: | 20uL, 100uL |
Isotype: | IgG |
Host Species: | Rabbit |
Reactivity: | Human,Mouse,Rat |
Immunogen: | A synthetic peptide corresponding to a sequence within amino acids 200-300 of human G6PC (NP_000142.2). |
Sequence: | SIYN ASLK KYFL ITFF LFSF AIGF YLLL KGLG VDLL WTLE KAQR WCEQ PEWV HIDT TPFA SLLK NLGT LFGL GLAL NSSM YRES CKGK LSKW LPFR LSSI V |
Tested Applications: | WB ELISA |
Recommended Dilution: | WB,1:1000 - 1:5000 |
Synonyms: | G6PC; G6PT; GSD1; GSD1a; G6Pase |
Positive Sample: | Huh-7 |
Conjugate: | Unconjugated |
Calculated MW: | 40kDa |
Observed MW: | 40kDa |
Glucose-6-phosphatase (G6Pase) is a multi-subunit integral membrane protein of the endoplasmic reticulum that is composed of a catalytic subunit and transporters for G6P, inorganic phosphate, and glucose. This gene (G6PC) is one of the three glucose-6-phosphatase catalytic-subunit-encoding genes in human: G6PC, G6PC2 and G6PC3. Glucose-6-phosphatase catalyzes the hydrolysis of D-glucose 6-phosphate to D-glucose and orthophosphate and is a key enzyme in glucose homeostasis, functioning in gluconeogenesis and glycogenolysis. Mutations in this gene cause glycogen storage disease type I (GSD1). This disease, also known as von Gierke disease, is a metabolic disorder characterized by severe hypoglycemia associated with the accumulation of glycogen and fat in the liver and kidneys.
Purification Method: | Affinity purification |
Gene ID: | 2538 |
Storage Buffer: | Store at -20℃. Avoid freeze / thaw cycles.Buffer: PBS with 0.05% proclin300,50% glycerol,pH7.3. |