FAH
FAH (fumarylacetoacetate hydrolase, also named fumarylacetoacetase) is a hydrolase that catalyses the final step of tyrosine breakdown. It converts fumarylacetoacetate into fumarate and acetoacetate, and loss of its activity is implicated in tyrosinemia type I. Browse Assay Genie's current range of FAH research reagents below, or read on for the biology behind the target.
FAH is the enzyme that catalyses the final step in the breakdown of the amino acid tyrosine. It acts on fumarylacetoacetate and converts it into fumarate and acetoacetate. Because it sits at the end of the pathway, its activity determines whether upstream intermediates are cleared or accumulate.
The FAH protein belongs to the FAH family and carries the EC number 3.7.1.2. The human FAH gene has mouse and rat orthologs, both named Fah, which allows the pathway to be studied in rodent systems. NCBI Gene summarises the protein as predicted to enable fumarylacetoacetase activity. It is also predicted to take part in several catabolic processes: L-tyrosine, L-phenylalanine and homogentisate catabolism. It is predicted to act upstream of or within L-arginine catabolism as well. The protein is annotated as located in extracellular exosomes.
Disease relevance is well defined: FAH is implicated in tyrosinemia type I. For researchers, this ties the enzyme to questions in amino acid metabolism, inherited metabolic disease and the biochemistry of tyrosine and phenylalanine degradation. An FAH antibody, FAH ELISA kit or recombinant FAH protein can support work on expression, abundance and function of this enzyme, and the FAH gene is a natural focus for studies of the tyrosine catabolic pathway.
FAH catalyses the final step of tyrosine breakdown, making it a key enzyme for investigating how this amino acid is degraded.
FAH is implicated in tyrosinemia type I, so it is a central target for studying this inherited metabolic disorder.
FAH is predicted to contribute to L-phenylalanine, homogentisate and L-arginine catabolic processes, linking several amino acid routes.
FAH is annotated as located in extracellular exosomes, which makes it relevant to studies of exosome-associated proteins.
FAH catalyses the final step in the breakdown of the amino acid tyrosine, converting fumarylacetoacetate into fumarate and acetoacetate. It is a hydrolase with the EC number 3.7.1.2 and belongs to the FAH family of proteins.
The HGNC full name is fumarylacetoacetate hydrolase, and UniProt names the protein fumarylacetoacetase. No other aliases or previous symbols are recorded in the data, so FAH is the standard symbol used for the gene and the protein.
FAH is implicated in tyrosinemia type I. Mouse and rat both have an ortholog named Fah, so rodent models can be used to study the gene. Check the datasheet of any product for its validated reactivity.
Other tyrosine pathway enzymes and amino acid metabolism targets with products at Assay Genie.
Gene and protein annotations from HGNC, NCBI Gene and UniProt P16930; product specifications from Assay Genie datasheets.